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Miopatia nemalinica pdf
Alguns casos possuem uma evolução benigna, com deformidades ósseas tardias. Disease definition. Nemaline myopathy (NM) encompasses a large spectrum of myopathies characterized by hypotonia, weakness and depressed or absent deep tendon reflexes, with pathologic evidence of nemaline bodies (rods) on muscle biopsy Miopatías nemalínicas: se caracterizan por la presencia de cuerpos o bastones nemalí-nicos. Miopatías centronucleares: antes también llamada “miopatía miotubular” PDF Nemaline myopathy is
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